see also: [[Haemolytic uraemic syndrome|HUS]], [[Thrombotic Thrombocytopaenic purpura|TTP]]
> **definition:** systemic pathological process that results in both thrombosis and haemorrhage initiated by a number of defined disorders
massive activation of clotting system → generalised activation of fibrinolytic system
![[12328D07-4D7E-4876-86BE-C0676AF0C7FF.jpeg]]
# causes
- Tissue damage (eg trauma, major surgery)
- [[Burns]]
- infection
- shock states in general
- malignancy
- [[Pre-eclampsia|Eclampsia]]
- [[placental abruption]]
- [[Snakebite]]
- severe pancreatitis
- [[amniotic fluid embolism]]
most common ED causes:
- sepsis
- massive blood loss
- major head injury
- snake bite
- eclampsia
- [[rhabdomyolysis]]
- [[Heat-related illness|Heat Stroke]]
> **mnemonic**:: HOTMISS
> - hepatic failure
> - obstetric
> - amniotic fluid embolism
> - eclampsia
> - fetal death in utero
> - trauma
> - malignancy
> - prostate, mucinous, APML
> - immune
> - [[Acute transfusion reactions]]
> - [[Anaphylaxis]]
> - [[Sepsis]]
> - gram negative
> - viral haemorrhagic fevers (eg [[Malaria]]
> - shock of other causes
# clinical features
1. suffering from a recognised cause of DIC
2. evidence of MODS:
1. multi-site bleeding
2. renal failure
3. hypotension
4. [[ARDS]]
5. ALOC
3. Lab evidence
# Lab investigations
![[Pasted image 20240219141140.png]]
^ from [rosen DIC](x-devonthink-item://F3C647AF-B411-4C79-AA85-8C42F04A7DFC?page=12&istart=1007&ilength=37&search=Disseminated%20Intravascular%20Coagulation)
> [!treatment] Ix
> - decreased fibrinogen levels
> - increased fibrin degredation products (↑ [[D-dimer]])
> - generally > 30
> - <2 unlikely to be DIC
> - increased thrombin time (reflects ongoing fibrinolysis)
> - low platelet levels
> - ↑ INR
> - ↑ APTT
> - decreased protein C
## DIC scoring system
| item | 0 | 1 point | 2 point | 3 points |
| ---------------- | ------ | ------- | ------------ | -------------- |
| plt count | >100 | 50-100k | <50k | - |
| d dimer | normal | | mod increase | large increase |
| prothrombin time | <3 s | 3-6s | ≥ 6s | |
| fibrinogen | ≥ 1 | <1 | | |
- ≥ 5 : suggests overt DIC
- <5 : suggests non-overt DIC
# Differences from TTP and HUS
- patients with TTP-HUS present with thrombocytopaenia and microangiopathic blood smere, but usually have normal levels of coagulation components and *little or no prolongation of PT or APTT* . the *fibrinogen levels* and D-dimer levels in TTP-HUS are also *normal*.
- TTP-HUS is initially treated with **plasma exchange**, but this is **NOT** the modality used to treat DIC
# Management
- supportive
- treat underlying cause
- +/- blood components
- fibrinogen <50 mg/dL need [[FFP]] or [[cryoprecipitate]] target fibrinogen >100mg/dL
- tx pts at high risk of bleeding
- [[thrombocytopaenia]] <50,000 mc/L need platelet transfusion