See also [[Anaemia]], [[haemolytic anaemia]]
> Microangiopathic hemolytic anemia is a direct [[Coombs test| antibody test-negative]] intravascular hemolysis caused by excessive shear or turbulence in the circulation. → fragmented RBCs (eg, triangles, helmet shapes) called *schistocytes*. Cause ↑ RBC distribution width
Disease of small blood vessels, resulting in haemolytic anaemia due to factors in small blood vessels. See *schistocytes* on blood film.
In all causes, ==the mechanism of MAHA is the formation of a fibrin mesh due to increased activation of the system of coagulation.== The red blood cells are physically cut by these protein networks. **The resulting fragments are the schistocytes observed in light microscopy**
Some MAHAs are associated with [[thrombocytopaenia]]
# causes
- [[DIC]]
- [[Pre-eclampsia#HELLP]]
- [[Thrombotic Thrombocytopaenic purpura|TTP]]
- [[Haemolytic uraemic syndrome|HUS]]
- Cancer
- Malignant hypertension
- cancer
- Antiphospholipid syndrome
- Chemo
- Polarteritis nodosa
- Granulomatosis with polyangiitis
# treatment
*Platelets and cryoprecipitate are contraindicated* as they facilitate further clot formation and RBC lysis.
Plasmapheresis is one treatment for TTP; corticosteroids should also be considered.